Special clinical nutrition formula of fatty acid metabolism disorder and preparation method thereof

Abstract

The invention provides a special clinical nutrition formula of fatty acid metabolism disorder. The nutrition formula is characterized by comprising, by weight, 15-28 parts of protein, 8-12 parts of fat, 48-65 parts of carbohydrate, 3-6 parts of dietary fiber, 0.6-1.2 parts of macro-elements, 0.01-0.04 part of microelement, 0.005-0.03 part of lipid-soluble vitamin, 0.08-0.2 part of water soluble vitamin, 0.06-2 parts of medicinal and edible components, 0.02-3 parts of natural plant compounds and 0.02-2 parts of new resource food; the invention further provides a preparation method of the aboveclinical nutrition formula. The formula can supplement nutrition required by patients suffering from fatty acid metabolism disorder, improve multi-fat metabolism disorder, promote normal fat metabolism, relieve fat metabolism disorder symptoms, and relieve pain of patients.

Description

technical field [0001] The invention relates to the field of nutritional formula, in particular to a special clinical nutritional formula for fatty acid metabolism abnormality and a preparation method thereof. Background technique [0002] Abnormal fatty acid metabolism (fatty acid metabolism disorder) is caused by the lack of fatty acid β-oxidase or transporter in the body, which leads to fatty acid decomposition and energy generation disorders, and abnormal functions of the nervous system, skeletal muscle, heart, liver, kidney, and digestive tract. The most common deficiency is medium-chain acyl-CoA dehydrogenase (MCAD). The disease is an inherited metabolic disease, mainly affecting infants and children, most of them begin within two years of birth, and there is often a family history. The clinical manifestations are chronic myasthenia, myalgia, or cardiomyopathy. It can also be manifested as fasting coma and hypoglycemia. During the onset, there are often no symptoms, a...

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Problems solved by technology

[0005] 2) CoA dehydrogenase (ACD) deficiency: including very long-chain, medium-chain, and short-chain ACD defects, and its frequent populations, clinical manifestations and gene mutations are different;

[0006] 3) Mitochondrial matrix β-oxidase deficiency: including long-chain and short-chain 3-hydroxyacyl-CoA dehydrogenase (LCHAD, SCHAD) deficiency; among them, SCHAD deficiency is relatively rare;

[0008] 5) Multiple energy metabolism defects: Multiple metabolic defects can act together to reduce production capacity, and the degree of reduction is consistent with the development of clinical symptoms, which is called synergistic heterogeneity

However, it has not been able to understand the pathogenesis of patients with abnormal lipid metabolism in different clinical manifestations for different clinical manifestations of abnormal lipid metabolism. Nutritional Formulas for Abnormal Symptoms